What is Pathology- Cystic Fibrosis
Pathophysiology Chromosome 7 is impacted by an autosomal recessive disease that prevents it from producing the protein CFTR, which regulates the movement of Na+ and Cl- ions. • perspiration glands do not reabsorb sodium, so salt depletion in perspiration can happen. • All exocrine secretions of the respiratory, gastrointestinal, and reproductive tracts thicken and obstruct normal flow. Evaluation and Diagnostic Results • Pancreatic enzymes for infants who appear with a meconium ileus and kids with recurrent or severe pulmonary disease; CXR; sweat electrolyte testing; PFTs; fat absorption. • Genetic testing of the kid and parents. Complications • Impaired exocrine activity of the pancreas. recurring gastritis and type 1 DM. • Potentially deadly recurrent respiratory infections and atelectasis; respiratory exertion may cause the thorax to resemble a barrel. • Bowel blockage, hypovitaminosis, malnutrition, and steatorrheic stools. • Stagnation. medical attention and surgical procedure • Enzymes from the pancreas. • Chest palpation, additional oxygen, antibiotics for respiratory episodes, ABG, CXR, and CBC. ● Lung reconstruction. • Genetic guidance. • The illness is persistent, and patients typically live shorter lives (3 or 4 decades). • It is necessary to keep replacing pancreas enzymes and pounding the chest. • Flu and pneumonia vaccinations are advised for people at elevated risk. • Track PFTs and O2 levels; listen to your lungs every four hours. • Check stools for blockage in the small intestine. • Check test results for hypovitaminosis and low protein levels. • Keep in mind: Support families mentally.
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8/11/2023 05:20:52 am
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